经超声心动图产前诊断胎儿肺动脉瓣缺如综合征12例分析
玉今珒;申俊君;蒋秋平;张旭;张智伟;潘微
【期刊名称】《中华围产医学杂志》 【年(卷),期】2018(021)003
【摘要】Objective To summarize the echocardiographic features of fetal absent pulmonary valve syndrome (APVS).Methods Clinical data and echocardiograms of 12 cases of fetal APVS prenatally diagnosed in the Department of Pediatric Cardiology,Guangdong Cardiovascular Institute from July 2015 to April 2017 were reviewed retrospectively and the echocardiographic
features
of
APVS
were
summarized.Results
Aneurysmal dilation of the main pulmonary artery and branches arteries were found in all cases,causing tracheal and esophageal compression in one case and lung compression in two cases.Color Doppler revealed systolic and diastolic turbulent blood flow with \and-fro\
blood flow
in
pulmonary
arteries
and
pulmonary
regurgitation.All fetuses were situs solitus and atrioventricular concordance.Eleven cases were also identified with malposition of the great arteries accompanied with ventricular septal defect,while the other one with normally related great arteries and intact ventricular septum was diagnosed with dysplasia of distal left pulmonary artery and
pericardial
effusion.Absent
ductus
arteriosus,increased
cardiothoracic ratio and myocardial hypertrophy were found in four,two